A biopsy of the lesions showed that these lesions were lngerhans with langerhans cell histiocytosis. Langerhans cell histiocytosis is a disorder in which excess immune system cells called langerhans cells build up in the body. Srj is a prestige metric based on the idea that not all citations are the same. Histiocitosis o enfermedades histiocitarias pediatria integral. Gomez am, lotero v, martinez p, medina d, ramirez o.
Langerhans cells, which help regulate the immune system, are normally found throughout the body, especially in the skin. Langerhans cell histiocytosis was first described in the 19th cen tury, and since then has been described with different names given its poorly known etiology. Any organ or system of the human body can be affected, but those more frequently involved are the skeleton 80% of cases, the skin 33%, and the pituitary 25%. Langerhans cell histiocytosis genetics home reference nih. Las celulas dendriticas comparten propiedades con monocitos y macrofagos, pero poseen distintiva citomorfologia. Abstract histiocytosis is a group of proliferative disorders, reactive or. It is characterized by the accumulation and proliferation of histiocytes, eosinophils and langerhans cells with birbeck granules detected by electron microscopy. Gastrointestinal involvement in langerhans cell histiocytosis. Langerhans cell histiocytosis lch is a heterogeneous disease, characterized by accumulation of dendritic cells with features similar to epidermal langerhans cells in various organs. A read is counted each time someone views a publication summary such as the title, abstract, and list of authors, clicks on a figure, or views or downloads the fulltext. Abstract langerhans cells histiocytosis lch is a systemic disorder presenting oral involvement, which can be the first lesion of this disease. Langerhans cell histiocytosis radiology reference article.
807 1470 1099 88 1499 1184 471 780 853 286 1065 1127 880 693 1200 1047 229 1516 613 277 704 74 261 383 1354 454 79 420 373 1411 769 347 1191 262 1171